Anaesthetic considerations in a child with fibrodysplasia ossificans progressiva

Authors

  • Thomas Kleyenstuber University of the Witwatersrand

Keywords:

airway management, fibreoptic intubation, fibrodysplasia ossificans progressiva, paediatric anaesthesia

Abstract

Fibrodysplasia ossificans progressiva (FOP) is an extremely rare genetic disorder characterised by extraskeletal ossification of connective tissue. Affected individuals often become completely immobilised by their third decade of life. Amongst numerous anaesthetic concerns, the airway management of patients with FOP may prove to be the greatest challenge. This case report describes the anaesthetic management of a three-year-old girl with FOP and highlights the difficulties encountered during airway management.

Author Biography

Thomas Kleyenstuber, University of the Witwatersrand

Department of Anaesthesia, Rahima Moosa Mother and Child Hospital, University of the Witwatersrand, Johannesburg, South Africa

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Published

2019-03-01

Issue

Section

Case Studies