Case Studies

Pentalogy of Cantrell and anaesthesia: a case report

Alexis Oosthuizen
Southern African Journal of Anaesthesia and Analgesia | Vol 23, No 5 | a1122 | DOI: https://doi.org/10.1080/22201181.2017.1355659 | © 2017 Alexis Oosthuizen | This work is licensed under Other
Submitted: 18 November 2025 | Published: 30 October 2016

About the author(s)

Alexis Oosthuizen, Department of Anaesthesia, Chris Hani Baragwanath Academic Hospital, Johannesburg, South Africa

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Abstract

Pentalogy of Cantrell, a rare congenital thoracoabdominal disruption, consists of a supraumbilical abdominal wall defect, lower sternal defect, agenesis of the anterior portion of the diaphragm, an absence of the diaphragmatic part of the pericardium, and a malformation of the heart, typically as an ectopia cordis. This case report presents a female neonate, 35 weeks postconception, weighing 2080 g who presented on day four of life for anaesthesia. She had the five anatomical defects characteristic of Pentalogy of Cantrell.

Keywords

abdominal wall defects; anaesthesia; congenital heart disease; ectopia cordis; extrathoracic heart; Pentalogy of Cantrell; perioperative management; transfer difficulties in South Africa

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Crossref Citations

1. Pentalogía de Cantrell. Reporte de un caso en el Hospital San Vicente de Paúl de Ibarra, Ecuador
V.J. Samaniego Haro
Clínica e Investigación en Ginecología y Obstetricia  vol: 48  issue: 1  first page: 36  year: 2021  
doi: 10.1016/j.gine.2020.09.005