Pentalogy of Cantrell and anaesthesia: a case report

  • Alexis Oosthuizen Chris Hani Baragwanath Academic Hospital
Keywords: abdominal wall defects, anaesthesia, congenital heart disease, ectopia cordis, extrathoracic heart, Pentalogy of Cantrell, perioperative management, transfer difficulties in South Africa


Pentalogy of Cantrell, a rare congenital thoracoabdominal disruption, consists of a supraumbilical abdominal wall defect, lower sternal defect, agenesis of the anterior portion of the diaphragm, an absence of the diaphragmatic part of the pericardium, and a malformation of the heart, typically as an ectopia cordis. This case report presents a female neonate, 35 weeks postconception, weighing 2080 g who presented on day four of life for anaesthesia. She had the five anatomical defects characteristic of Pentalogy of Cantrell. (Full text available online at South Afr J Anaesth Analg 2017; DOI: 10.1080/22201181.2017.1355659

Author Biography

Alexis Oosthuizen, Chris Hani Baragwanath Academic Hospital
Department of Anaesthesia Chris Hani Baragwanath Academic Hospital Johannesburg South Africa
Case Studies