Anaesthesia for left thoracoscopic sympathectomy for refractory long QT syndrome: three case reports

  • Madhusudan Upadya Manipal University
  • Julie C R Misquith Manipal University
  • Rammoorthi Rao Manipal University
Keywords: congenital condition, left cardiac sympathetic denervation, left thoracic sympathectomy, prolonged QT syndrome, video-assisted thoracoscopic surgery

Abstract

Congenital long QT syndrome (LQTS) is a rare genetic disorder that has been associated with various genetic mutations including life-threatening cardiac arrhythmias and sudden death. Left thoracoscopic sympathectomy is an effective treatment for patients who are refractory to medical therapy or who need frequent epicardial internal cardio defibrillator intervention. The authors report three cases, one adult and two children, who underwent successful left thoracoscopic sympathectomy. All three patients remained clinically stable without arrhythmias through 3 months of follow-up. It is suggested in the literature that 77% of patients experienced immediate relief of symptoms. The results of this case report suggest that left thoracoscopic sympathectomy is a safe and effective approach for treating patients with LQTS. (Full text available online at www.medpharm.tandfonline.com/ojaa) South Afr J Anaesth Analg 2016; DOI: 10.1080/22201181.2016.1223924

Author Biographies

Madhusudan Upadya, Manipal University
Department of Anaesthesia Kasturba Medical College Manipal University Mangalore India
Julie C R Misquith, Manipal University
Department of Anaesthesia Kasturba Medical College Manipal University Mangalore India
Rammoorthi Rao, Manipal University
Department of Anaesthesia Kasturba Medical College Manipal University Mangalore India
Published
2016-11-07
Section
Case Studies